Herlyn-Werner-Wunderlich: A Rare Disease
DOI:
https://doi.org/10.56951/b65m7m40Kata Kunci:
Herlyn-Werner-Wunderlich, rare disease, uterus didelphysAbstrak
Herlyn-Werner-Wunderlich (HWW) is a rare Mullerian disorder characterized by uterine didelphys, hemivaginal obstruction, and ipsilateral renal agenesis. This paper aimed to describe a rare case of HWW in order to give better understanding of the disease, as well as diagnosis and treatment. Then urgent action is taken in the form of incision and drainage of pus. Methods: We searched medical record of a 17-year-old girl complaining of vaginal pain since menarche. Ultrasound examination found hematocolpos and vaginal septum, pelvic MRI found uterus didelphys and left renal agenesis, then the septal incision was performed to facilitate pus drainage. Conclusion: Herlyn-Werner-Wunderlich is a rare condition with varying age of onset. Anamnesis, physical examination, ultrasonography, and MRI are needed to confirm diagnosis. As an urgent measure, a septal incision and pus drainage are performed to reduce symptoms and complications that could occur in the future. In addition, the patient needs to undergo septal resection as a follow-up treatment which can only be done in a hospital where urogenital and reconstruction divisions are available.
Unduhan
Referensi
Sanfilippo JS, Lara-Torre E, Gomez-Lobo V. Sanfilippo’s Textbook of Pediatric And Adolescent Gynecology. CRC Press; 2019.p.90. DOI: https://doi.org/10.1201/9781315147659
Pfeifer SM (Eds). Congenital Müllerian Anomalies. Springer. Switzerland: Springer Nature; 2016.p.133–8. DOI: https://doi.org/10.1007/978-3-319-27231-3
Amesse LS. Mullerian Duct Anomalies. Available from: https://emedicine.medscape.com/article/273534-overview#a1?form=fpf cited Oct 22, 2022.
Fulghesu AM (Eds). Good practice in pediatric and adolescent gynecology. Springer. Cagliari: Springer Nature; 2018.p.45-9. DOI: https://doi.org/10.1007/978-3-319-57162-1
Dietrich J, Ponsky TA, Sanfilippo J (Eds). Endometriosis in Adolescents. Springer. Switzerland: Springer Nature Switzerland AG; 2020.p.263-78.
Wang J, Zhu L, Lang J, Liu Z, Sun D, Leng J, et al. Clinical characteristics and treatment of Herlyn-Werner-Wunderlich syndrome, Arch Gynecol Obstet. 2014;290(5):947-50.
Wang J, Zhu L, Lang J, Liu Z, Sun D, Leng J, et al. Clinical characteristics and treatment of Herlyn-Werner-Wunderlich syndrome, Arch Gynecol Obstet. 2014;290(5):947-50. DOI: https://doi.org/10.1007/s00404-014-3286-5
Tong J, Zhu L, and Lang J. Clinical characteristics of 70 patients with Herlyn–Werner–Wunderlich syndrome. International Journal of Gynecology & Obstetrics 2013;121(2):173-5. DOI: https://doi.org/10.1016/j.ijgo.2012.11.023
Chai JL and Burk KS. Congenital uterine anomalies. Available from: https://rad.bwh.harvard.edu/congenital-uterine-anomalies cited Oct 22, 2022.
Zhu L, Chen N, Tong J, Zhang L, Lang J. New classification of Herlyn-Werner-Wunderlich syndrome Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4837842/ cited Nov 15, 2022.
Witrianti RD, Iman N, Fajarini ES. Peranan MRI abdomen pada kasus Herlyn-Werner-Wunderlich. Jurnal Radiografer Indonesia 2020;3(1):42-5. DOI: https://doi.org/10.55451/jri.v3i1.64
Sidhu HS, Madaan PK. Herlyn-Werner-Wunderlich syndrome in a multiparous female [Internet]. 2020 [cited 2022 Oct 22]. Available from: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7869122/
Wang J, Zhu L, and Lang J. Clinical characteristics and treatment of Herlyn–werner–wunderlich syndrome. BJR Case Rep. 2020;7(1):20200132. DOI: https://doi.org/10.1259/bjrcr.20200132
Grimbizis GF, Camus M, Tarlatzis BC, Bontis JN, Devroey P. Clinical implications of uterine malformations and hysteroscopic treatment results. Hum Reprod Update. 2001;7(2):161-74. DOI: https://doi.org/10.1093/humupd/7.2.161
Boyraz G, Karalok A, Turan T, Özgül N. Herlyn-Werner-Wunderlich syndrome; laparoscopic treatment of obstructing longitudinal vaginal septum in patients with hematocolpos - a different technique for virgin patients. J Turk Ger Gynecol Assoc. 2020;21(4):303–4. DOI: https://doi.org/10.4274/jtgga.galenos.2019.2019.0046
Fachin CG, Rocha JLAS, Maltoni AA, Lima RLC, Zendim VA, Agulham MA, et al. Herlyn-Werner-Wunderlich syndrome: Diagnosis and treatment of an atypical case and review of literature. Int J Surg Case Rep. 2019:63:129-34. DOI: https://doi.org/10.1016/j.ijscr.2019.08.035
Unduhan
Terbitan
Bagian
Diterbitkan
Unduhan
Lisensi
Hak Cipta (c) 2023 Yoki Citra Perwira, Jeffy Winarya Wahyudi
Artikel ini berlisensi Creative Commons Attribution-NonCommercial 4.0 International License.
Cara Mengutip
